Heterotaxy syndrome with intestinal malrotation, polysplenia and azygos continuity
Abstract
Heterotaxy syndrome is a situs anomaly that comprises a large spectrum of cardiac and extracardiac malformations. Its association with intestinal malrotation is frequent. This later might be asymptomatic or manifest by signs of abdominal discomfort or of intestinal obstruction. We report on the case of a full term, small for gestational age neonate in whom heterotaxy syndrome with partial situs inversus abdominalis, intestinal malrotation, polysplenia and vena azygos continuity was diagnosed at prenatal echography. Due to the high risk of volvulus carried by the malrotation, Ladd’s procedure was performed at the age of two months. Follow-up examination at the age of four years shows excellent post-operative result and normal development of the child.Downloads
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Published
2018-01-08
Keywords:
Heterotaxy, intestinal malrotation, azygos continuity.
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How to Cite
Cupers, S., Van Linthout, C., Desprechins, B., Rausin, L., Demarche, M., & Seghaye, M.-C. (2018). Heterotaxy syndrome with intestinal malrotation, polysplenia and azygos continuity. Clinics and Practice, 8(1). https://doi.org/10.4081/cp.2018.1004
Copyright (c) 2018 Stéphanie Cupers, Christine Van Linthout, Brigitte Desprechins, Léon Rausin, Martine Demarche, Marie-Christine Seghaye

This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.