Giant adrenal cavernous hemangioma in a patient with familial adenomatous polyposis

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Dhouha Bacha *
Abir Chaabane
Fatma Khanchel
Saloua Néchi
Hassen Touinsi
Emna Chelbi
(*) Corresponding Author:
Dhouha Bacha | dhouhabacha@gmail.com

Abstract

Adrenal hemangioma is an uncommon benign vascular tumor that is often discovered incidentally. It has never been reported in association with familial adenomatous polyposis. We report a case of a 60-year old man with a history of familial adenomatous polyposis, in whom a huge retroperitoneal cyst of 18×17 cm was discovered during routine radiologic evaluation. Because of the impossibility of ruling out the presence of malignancy, surgical cystectomy was performed, associated to a scheduled total colectomy. Pathological examination revealed that the cyst corresponded to an adrenal cavernous hemangioma. Colonic adenomas did not show signs of degeneration. Screening for adenomatous polyposis coli (APC) gene mutation was not carried out. As familial adenomatous polyposis is known to involve a variety of extracolonic manifestations, this finding raises the suspicion of a possible variant of this syndrome including adrenal hemangioma. An extensive study based on a larger patient series with genetic exploration is necessary.

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Author Biographies

Dhouha Bacha, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis

Pathology Department, Mongi Slim Hospital, Tunis, Tunisia

University assistant

 

Abir Chaabane, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis

Pathology Department, Med Tahar Maamouri Hospital

Fatma Khanchel, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis

Pathology Department, Med Tahar Maamouri Hospital

Saloua Néchi, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis

Pathology Department, Med Tahar Maamouri Hospital

Hassen Touinsi, Surgery Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis

Surgery Department, Med Tahar Maamouri Hospital

University Professor

Emna Chelbi, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis

Pathology Department, Med Tahar Maamouri Hospital