Giant adrenal cavernous hemangioma in a patient with familial adenomatous polyposis

  • Dhouha Bacha | dhouhabacha@gmail.com Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis, Tunisia.
  • Abir Chaabane Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis, Tunisia.
  • Fatma Khanchel Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis, Tunisia.
  • Saloua Néchi Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis, Tunisia.
  • Hassen Touinsi Surgery Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis, Tunisia.
  • Emna Chelbi Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis, Tunisia.

Abstract

Adrenal hemangioma is an uncommon benign vascular tumor that is often discovered incidentally. It has never been reported in association with familial adenomatous polyposis. We report a case of a 60-year old man with a history of familial adenomatous polyposis, in whom a huge retroperitoneal cyst of 18×17 cm was discovered during routine radiologic evaluation. Because of the impossibility of ruling out the presence of malignancy, surgical cystectomy was performed, associated to a scheduled total colectomy. Pathological examination revealed that the cyst corresponded to an adrenal cavernous hemangioma. Colonic adenomas did not show signs of degeneration. Screening for adenomatous polyposis coli (APC) gene mutation was not carried out. As familial adenomatous polyposis is known to involve a variety of extracolonic manifestations, this finding raises the suspicion of a possible variant of this syndrome including adrenal hemangioma. An extensive study based on a larger patient series with genetic exploration is necessary.

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Author Biographies

Dhouha Bacha, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis

Pathology Department, Mongi Slim Hospital, Tunis, Tunisia

University assistant

 

Abir Chaabane, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis
Pathology Department, Med Tahar Maamouri Hospital
Fatma Khanchel, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis
Pathology Department, Med Tahar Maamouri Hospital
Saloua Néchi, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis
Pathology Department, Med Tahar Maamouri Hospital
Hassen Touinsi, Surgery Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis

Surgery Department, Med Tahar Maamouri Hospital

University Professor

Emna Chelbi, Pathology Department, Med Tahar Maamouri Hospital, Tunis El Manar University, Tunis
Pathology Department, Med Tahar Maamouri Hospital
Published
2016-10-10
Section
Case Reports
Keywords:
Hemangioma, cavernous, adrenal gland, familial adenomatous polyposis.
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How to Cite
Bacha, D., Chaabane, A., Khanchel, F., Néchi, S., Touinsi, H., & Chelbi, E. (2016). Giant adrenal cavernous hemangioma in a patient with familial adenomatous polyposis. Clinics and Practice, 6(3). https://doi.org/10.4081/cp.2016.878